Operative Planning in Esophageal Atresia With Right Arch-Based Vascular Rings: A Referral-Center Experience.

Twenty-four patients were identified (83% type C esophageal atresia).

Vascular ring subtypes included right aortic arch with aberrant left subclavian artery (RAA+ALSCA 71%), double aortic arch (17%), and right aortic arch with left ligamentum (13%).

Echocardiography was concordant with operative findings in 70%, discordant in 10%, and missed a vascular ring in 20%.

Referred patients had prior or active leak (42%), refractory stricture (60%), recurrent fistula (28%), dysphagia (90%), and vocal fold movement impairment (53%).