Protein-losing enteropathy after the Fontan procedure - A cardiologist's and gastroenterologist's perspective.

ReviewAnnals of pediatric cardiology· 2026

Protein-losing enteropathy after the Fontan procedure - A cardiologist's and gastroenterologist's perspective.

Natalia Nawara-Węgrzyn, Łukasz Cichy, Kinga Kowalska-Duplaga, Aleksandra Morka

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Congenital Cardiac SurgeryReviewTreatmentQ3IF 0.7

Protein-losing enteropathy complicates Fontan circulation in about 1 in 8 patients

Protein-losing enteropathy after the Fontan procedure - A cardiologist's and gastroenterologist's perspective.

Natalia Nawara-Węgrzyn … Aleksandra Morka

Annals of pediatric cardiology · 2026

Results

12%

nearly 1 in 8 with a single-ventricle heart develop this complication

More results

When conservative and interventional strategies fail, heart transplantation remains the definitive option.

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Conclusion

This review summarizes current concepts in protein-losing enteropathy pathophysiology and therapeutic approaches, with emphasis on lymphatic dysfunction and evolving adjunctive targets.

Protein-losing enteropathy after the Fontan procedure - A cardiologist's and gastroenterologist's perspective.

Protein-losing enteropathy after the Fontan procedure - A cardiologist's and gastroenterologist's perspective.

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