Papilledema and Pseudopapilledema in Alagille Syndrome: A Case Report.

Neuro-ophthalmic findings include optic disc swelling and cerebral vascular anomalies.

Here, we discuss the care of a lean young man with alagille syndrome and extreme optic disc swelling.

He had significant systemic co-morbidities, in the form of renal failure and anticoagulation after cardiac surgery.

Cerebrospinal fluid shunting was deemed unwise, due to the high revision rate which so often follows.