Clinicopathological characteristics and outcomes of 42 cases of ocular adnexal sarcoma.
Over a third of ocular adnexal sarcoma patients died during follow-up
Clinicopathological characteristics and outcomes of 42 cases of ocular adnexal sarcoma.
To study the clinicopathological features, treatment, and prognosis of ocular adnexal sarcomas diagnosed at a tertiary comprehensive hospital in China during 13 years.
A case series of patients with histopathological diagnoses of ocular adnexal sarcomas at a tertiary general hospital over 13 years.
The mean age was 37.1 years, with 27 males and 15 females.
The most common clinical manifestation was exophthalmos (61.9%), and the median time to diagnosis was 6 months.
These tumors most often occurred in the orbit (83.3%).
The most common TNM stage at presentation was T2N0M0 (63.6%).
Ocular adnexal sarcomas are rare and histologically diverse, with rhabdomyosarcoma predominating in children and liposarcoma and malignant solitary fibrous tumor in adults.
Middle-aged and elderly patients presenting with unilateral proptosis accompanied by visual impairment, especially in cases of cranio-orbital communication associated with headache, should raise suspicion for the possibility of malignant solitary fibrous tumor to avoid delayed diagnosis.